PackagesCanonicalsLogsProblems
    Packages
    us.nlm.vsac@0.17.0
    http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113762.1.4.1248.91
{
  "description": "ICD10 codes listed are from PSI 11 Neuromuscular disorder diagnosis codes: (NEUROMD)",
  "compose": {
    "include": [ {
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "concept": [ {
        "code": "E74.02",
        "display": "Pompe disease"
      }, {
        "code": "G12.1",
        "display": "Other inherited spinal muscular atrophy"
      }, {
        "code": "G12.20",
        "display": "Motor neuron disease, unspecified"
      }, {
        "code": "G12.21",
        "display": "Amyotrophic lateral sclerosis"
      }, {
        "code": "G12.22",
        "display": "Progressive bulbar palsy"
      }, {
        "code": "G12.23",
        "display": "Primary lateral sclerosis"
      }, {
        "code": "G12.24",
        "display": "Familial motor neuron disease"
      }, {
        "code": "G12.25",
        "display": "Progressive spinal muscle atrophy"
      }, {
        "code": "G12.29",
        "display": "Other motor neuron disease"
      }, {
        "code": "G12.8",
        "display": "Other spinal muscular atrophies and related syndromes"
      }, {
        "code": "G12.9",
        "display": "Spinal muscular atrophy, unspecified"
      }, {
        "code": "G14",
        "display": "Postpolio syndrome"
      }, {
        "code": "G61.0",
        "display": "Guillain-Barre syndrome"
      }, {
        "code": "G70.00",
        "display": "Myasthenia gravis without (acute) exacerbation"
      }, {
        "code": "G70.01",
        "display": "Myasthenia gravis with (acute) exacerbation"
      }, {
        "code": "G70.1",
        "display": "Toxic myoneural disorders"
      }, {
        "code": "G70.2",
        "display": "Congenital and developmental myasthenia"
      }, {
        "code": "G70.80",
        "display": "Lambert-Eaton syndrome, unspecified"
      }, {
        "code": "G70.81",
        "display": "Lambert-Eaton syndrome in disease classified elsewhere"
      }, {
        "code": "G70.89",
        "display": "Other specified myoneural disorders"
      }, {
        "code": "G70.9",
        "display": "Myoneural disorder, unspecified"
      }, {
        "code": "G71.0",
        "display": "Muscular dystrophy"
      }, {
        "code": "G71.00",
        "display": "Muscular dystrophy, unspecified"
      }, {
        "code": "G71.01",
        "display": "Duchenne or Becker muscular dystrophy"
      }, {
        "code": "G71.02",
        "display": "Facioscapulohumeral muscular dystrophy"
      }, {
        "code": "G71.09",
        "display": "Other specified muscular dystrophies"
      }, {
        "code": "G71.11",
        "display": "Myotonic muscular dystrophy"
      }, {
        "code": "G71.12",
        "display": "Myotonia congenita"
      }, {
        "code": "G71.13",
        "display": "Myotonic chondrodystrophy"
      }, {
        "code": "G71.19",
        "display": "Other specified myotonic disorders"
      }, {
        "code": "G71.2",
        "display": "Congenital myopathies"
      }, {
        "code": "G71.20",
        "display": "Congenital myopathy, unspecified"
      }, {
        "code": "G71.21",
        "display": "Nemaline myopathy"
      }, {
        "code": "G71.220",
        "display": "X-linked myotubular myopathy"
      }, {
        "code": "G71.228",
        "display": "Other centronuclear myopathy"
      }, {
        "code": "G71.29",
        "display": "Other congenital myopathy"
      }, {
        "code": "G71.3",
        "display": "Mitochondrial myopathy, not elsewhere classified"
      }, {
        "code": "G71.8",
        "display": "Other primary disorders of muscles"
      }, {
        "code": "G71.9",
        "display": "Primary disorder of muscle, unspecified"
      }, {
        "code": "G72.0",
        "display": "Drug-induced myopathy"
      }, {
        "code": "G72.1",
        "display": "Alcoholic myopathy"
      }, {
        "code": "G72.2",
        "display": "Myopathy due to other toxic agents"
      }, {
        "code": "G72.3",
        "display": "Periodic paralysis"
      }, {
        "code": "G72.41",
        "display": "Inclusion body myositis [IBM]"
      }, {
        "code": "G72.49",
        "display": "Other inflammatory and immune myopathies, not elsewhere classified"
      }, {
        "code": "G72.81",
        "display": "Critical illness myopathy"
      }, {
        "code": "G72.89",
        "display": "Other specified myopathies"
      }, {
        "code": "G72.9",
        "display": "Myopathy, unspecified"
      }, {
        "code": "G73.1",
        "display": "Lambert-Eaton syndrome in neoplastic disease"
      }, {
        "code": "G73.3",
        "display": "Myasthenic syndromes in other diseases classified elsewhere"
      }, {
        "code": "G73.7",
        "display": "Myopathy in diseases classified elsewhere"
      }, {
        "code": "M05.40",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified site"
      }, {
        "code": "M05.411",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of right shoulder"
      }, {
        "code": "M05.412",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of left shoulder"
      }, {
        "code": "M05.419",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified shoulder"
      }, {
        "code": "M05.421",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of right elbow"
      }, {
        "code": "M05.422",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of left elbow"
      }, {
        "code": "M05.429",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified elbow"
      }, {
        "code": "M05.431",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of right wrist"
      }, {
        "code": "M05.432",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of left wrist"
      }, {
        "code": "M05.439",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified wrist"
      }, {
        "code": "M05.441",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of right hand"
      }, {
        "code": "M05.442",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of left hand"
      }, {
        "code": "M05.449",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified hand"
      }, {
        "code": "M05.451",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of right hip"
      }, {
        "code": "M05.452",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of left hip"
      }, {
        "code": "M05.459",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified hip"
      }, {
        "code": "M05.461",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of right knee"
      }, {
        "code": "M05.462",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of left knee"
      }, {
        "code": "M05.469",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified knee"
      }, {
        "code": "M05.471",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of right ankle and foot"
      }, {
        "code": "M05.472",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of left ankle and foot"
      }, {
        "code": "M05.479",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified ankle and foot"
      }, {
        "code": "M05.49",
        "display": "Rheumatoid myopathy with rheumatoid arthritis of multiple sites"
      }, {
        "code": "M33.01",
        "display": "Juvenile dermatomyositis with respiratory involvement"
      }, {
        "code": "M33.11",
        "display": "Other dermatomyositis with respiratory involvement"
      }, {
        "code": "M33.21",
        "display": "Polymyositis with respiratory involvement"
      }, {
        "code": "M33.91",
        "display": "Dermatopolymyositis, unspecified with respiratory involvement"
      }, {
        "code": "M34.82",
        "display": "Systemic sclerosis with myopathy"
      }, {
        "code": "M35.03",
        "display": "Sjögren syndrome with myopathy"
      }, {
        "code": "M41.40",
        "display": "Neuromuscular scoliosis, site unspecified"
      }, {
        "code": "M41.41",
        "display": "Neuromuscular scoliosis, occipito-atlanto-axial region"
      }, {
        "code": "M41.42",
        "display": "Neuromuscular scoliosis, cervical region"
      }, {
        "code": "M41.43",
        "display": "Neuromuscular scoliosis, cervicothoracic region"
      }, {
        "code": "M41.44",
        "display": "Neuromuscular scoliosis, thoracic region"
      }, {
        "code": "M41.45",
        "display": "Neuromuscular scoliosis, thoracolumbar region"
      }, {
        "code": "M41.46",
        "display": "Neuromuscular scoliosis, lumbar region"
      }, {
        "code": "M41.47",
        "display": "Neuromuscular scoliosis, lumbosacral region"
      } ]
    } ]
  },
  "_filename": "ValueSet-2.16.840.1.113762.1.4.1248.91.json",
  "package_name": "us.nlm.vsac",
  "date": "2023-09-23T01:01:29-04:00",
  "meta": {
    "profile": [ "http://hl7.org/fhir/StructureDefinition/shareablevalueset", "http://hl7.org/fhir/us/cqfmeasures/StructureDefinition/publishable-valueset-cqfm" ],
    "versionId": "10",
    "lastUpdated": "2023-11-21T16:21:22.000-05:00"
  },
  "publisher": "American Institutes for Research Steward",
  "jurisdiction": [ {
    "coding": [ {
      "code": "US",
      "system": "urn:iso:std:iso:3166"
    } ]
  } ],
  "purpose": "(Clinical Focus: The purpose of this value set is to represent concepts for neuromuscular disorders),(Data Element Scope: This value set may use a model element related to Diagnosis or Condition),(Inclusion Criteria: Includes concepts that represent neuromuscular disorders such as Guillain-Barre syndrome, myasthenia gravis, myasthenia, Lambert-Eaton syndrome, muscular dystrophy, myotonic disorders, myopathies, and myositis),(Exclusion Criteria: N/A)",
  "name": "NeuromuscularDisorder",
  "type": null,
  "experimental": null,
  "resourceType": "ValueSet",
  "expansion": {
    "total": 88,
    "contains": [ {
      "code": "E74.02",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Pompe disease",
      "version": "2024"
    }, {
      "code": "G12.1",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other inherited spinal muscular atrophy",
      "version": "2024"
    }, {
      "code": "G12.20",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Motor neuron disease, unspecified",
      "version": "2024"
    }, {
      "code": "G12.21",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Amyotrophic lateral sclerosis",
      "version": "2024"
    }, {
      "code": "G12.22",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Progressive bulbar palsy",
      "version": "2024"
    }, {
      "code": "G12.23",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Primary lateral sclerosis",
      "version": "2024"
    }, {
      "code": "G12.24",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Familial motor neuron disease",
      "version": "2024"
    }, {
      "code": "G12.25",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Progressive spinal muscle atrophy",
      "version": "2024"
    }, {
      "code": "G12.29",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other motor neuron disease",
      "version": "2024"
    }, {
      "code": "G12.8",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other spinal muscular atrophies and related syndromes",
      "version": "2024"
    }, {
      "code": "G12.9",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Spinal muscular atrophy, unspecified",
      "version": "2024"
    }, {
      "code": "G14",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Postpolio syndrome",
      "version": "2024"
    }, {
      "code": "G61.0",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Guillain-Barre syndrome",
      "version": "2024"
    }, {
      "code": "G70.00",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myasthenia gravis without (acute) exacerbation",
      "version": "2024"
    }, {
      "code": "G70.01",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myasthenia gravis with (acute) exacerbation",
      "version": "2024"
    }, {
      "code": "G70.1",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Toxic myoneural disorders",
      "version": "2024"
    }, {
      "code": "G70.2",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Congenital and developmental myasthenia",
      "version": "2024"
    }, {
      "code": "G70.80",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Lambert-Eaton syndrome, unspecified",
      "version": "2024"
    }, {
      "code": "G70.81",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Lambert-Eaton syndrome in disease classified elsewhere",
      "version": "2024"
    }, {
      "code": "G70.89",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other specified myoneural disorders",
      "version": "2024"
    }, {
      "code": "G70.9",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myoneural disorder, unspecified",
      "version": "2024"
    }, {
      "code": "G71.0",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Muscular dystrophy",
      "version": "2024"
    }, {
      "code": "G71.00",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Muscular dystrophy, unspecified",
      "version": "2024"
    }, {
      "code": "G71.01",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Duchenne or Becker muscular dystrophy",
      "version": "2024"
    }, {
      "code": "G71.02",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Facioscapulohumeral muscular dystrophy",
      "version": "2024"
    }, {
      "code": "G71.09",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other specified muscular dystrophies",
      "version": "2024"
    }, {
      "code": "G71.11",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myotonic muscular dystrophy",
      "version": "2024"
    }, {
      "code": "G71.12",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myotonia congenita",
      "version": "2024"
    }, {
      "code": "G71.13",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myotonic chondrodystrophy",
      "version": "2024"
    }, {
      "code": "G71.19",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other specified myotonic disorders",
      "version": "2024"
    }, {
      "code": "G71.2",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Congenital myopathies",
      "version": "2024"
    }, {
      "code": "G71.20",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Congenital myopathy, unspecified",
      "version": "2024"
    }, {
      "code": "G71.21",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Nemaline myopathy",
      "version": "2024"
    }, {
      "code": "G71.220",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "X-linked myotubular myopathy",
      "version": "2024"
    }, {
      "code": "G71.228",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other centronuclear myopathy",
      "version": "2024"
    }, {
      "code": "G71.29",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other congenital myopathy",
      "version": "2024"
    }, {
      "code": "G71.3",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Mitochondrial myopathy, not elsewhere classified",
      "version": "2024"
    }, {
      "code": "G71.8",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other primary disorders of muscles",
      "version": "2024"
    }, {
      "code": "G71.9",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Primary disorder of muscle, unspecified",
      "version": "2024"
    }, {
      "code": "G72.0",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Drug-induced myopathy",
      "version": "2024"
    }, {
      "code": "G72.1",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Alcoholic myopathy",
      "version": "2024"
    }, {
      "code": "G72.2",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myopathy due to other toxic agents",
      "version": "2024"
    }, {
      "code": "G72.3",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Periodic paralysis",
      "version": "2024"
    }, {
      "code": "G72.41",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Inclusion body myositis [IBM]",
      "version": "2024"
    }, {
      "code": "G72.49",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other inflammatory and immune myopathies, not elsewhere classified",
      "version": "2024"
    }, {
      "code": "G72.81",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Critical illness myopathy",
      "version": "2024"
    }, {
      "code": "G72.89",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Other specified myopathies",
      "version": "2024"
    }, {
      "code": "G72.9",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myopathy, unspecified",
      "version": "2024"
    }, {
      "code": "G73.1",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Lambert-Eaton syndrome in neoplastic disease",
      "version": "2024"
    }, {
      "code": "G73.3",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myasthenic syndromes in other diseases classified elsewhere",
      "version": "2024"
    }, {
      "code": "G73.7",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Myopathy in diseases classified elsewhere",
      "version": "2024"
    }, {
      "code": "M05.40",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified site",
      "version": "2024"
    }, {
      "code": "M05.411",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of right shoulder",
      "version": "2024"
    }, {
      "code": "M05.412",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of left shoulder",
      "version": "2024"
    }, {
      "code": "M05.419",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified shoulder",
      "version": "2024"
    }, {
      "code": "M05.421",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of right elbow",
      "version": "2024"
    }, {
      "code": "M05.422",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of left elbow",
      "version": "2024"
    }, {
      "code": "M05.429",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified elbow",
      "version": "2024"
    }, {
      "code": "M05.431",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of right wrist",
      "version": "2024"
    }, {
      "code": "M05.432",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of left wrist",
      "version": "2024"
    }, {
      "code": "M05.439",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified wrist",
      "version": "2024"
    }, {
      "code": "M05.441",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of right hand",
      "version": "2024"
    }, {
      "code": "M05.442",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of left hand",
      "version": "2024"
    }, {
      "code": "M05.449",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified hand",
      "version": "2024"
    }, {
      "code": "M05.451",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of right hip",
      "version": "2024"
    }, {
      "code": "M05.452",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of left hip",
      "version": "2024"
    }, {
      "code": "M05.459",
      "system": "http://hl7.org/fhir/sid/icd-10-cm",
      "display": "Rheumatoid myopathy with rheumatoid arthritis of unspecified hip",
      "version": "2024"
    }, {
      "code": "M05.461",
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